Abstract
Background:
CREST is an autoimmune disease characterized by vascular dysfunction and alterations in the microvasculature, culminating in ischemia and fibrosis of different tissues and organs. The prognosis of this rheumatic pathology will mainly depend on the degree of pulmonary, cardiac, and renal involvement.
The case:
We present the case of a 39-year-old female who presented with 20-day history of lower limb edema, Raynaud’s phenomenon, dyspnea on small exertions, and non-quantified fever with chills and sweating. On physical examination: presence of hyperchromic lesions on the back of both hands, accompanied by induration of the skin and multiple telangiectasias, foveal edema of the lower limbs (++) and hyperchromic lesions, indurated on the back of both feet. Anti-SCL70: positive, esophagogram: esophageal dysmotility, echocardiogram: corpulmonale and moderate pulmonary hypertension.
Conclusion:
This is an interesting and peculiar case, since he presented corpulmonale, and his evolution was satisfactory, without complications.
Received: 15/02/2020
Accepted: 10/03/2020
This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.
Copyright (c) 2022 Carlos Fernando Avilez Soto, Josué Degrandes Rodríguez