Morris Syndrom. Case report
DOI:
https://doi.org/10.18004/Keywords:
Morris Syndrom, amenorrhea, androgenic insensitivity, ParaguayAbstract
Androgen Insensitivity Syndrome is a form of male pseudohermaphroditism in which the target organs are unable to respond to testosterone or dihydrotestosterone. As a result, although the gonads are testes, genitalia virilization do not properly occurs during fetal development. The clinical manifestations varies from female genitalia in patients with complete androgen resistance or Morris syndrome; ambiguous genitalia in partial resistance or Reifenstein syndrome; to normal male genitalia in cases of milder forms of androgen resistance.
This is a case report of an adult woman who is attended at the Service of Obstetrics and Gynecology of the School of Medicine of the Universidad Nacional de Asunción. She wishes for a better sexual life. The patient is known to have Morris syndrome since 2006. Surgery is performed to expand the vagina, obtaining favorable results as it was confirmed in the follow up.
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