Systemic vasculitis with cutaneous involvement, in the Department of Dermatology, Faculty of Medical Sciences, National University of Asuncion
DOI:
https://doi.org/10.18004/anales/2017.050(02)23-034Keywords:
systemic vasculitis, cutaneous vasculitis, epidemiology, ParaguayAbstract
Introduction: Systemic vasculitis has multiple and varied organ involvement; Ranging from benign to deadly. Its clinical manifestations, treatment and prognosis will depend on the vessel involved, and on the extent and location of the lesion. Objectives: To determine epidemiological, clinical, and histopathological characteristics, and the treatment of systemic vasculitis with cutaneous manifestations in the Department of Dermatology Hospital of Clinics, FCM-UNA. Materials and Methods: A descriptive, observational, retrospective, cross-sectional study with an analytical component from January 2004 to December 2015. A spreadsheet was drawn up to record the variables obtained from clinical and histopathological records. Results: We found 11 patients with systemic vasculitis with cutaneous involvement, (0,0098% of the consultations). The male sex predominated (63,63%). The mean age was 30.18 years. 18,18% were children, all of them male. The most frequent elemental lesion was the papule (72,72%), the predominant location, lower limbs (72,72%). The most frequent symptoms were abdominal pain (63,63%) and arthralgia (54,54%). The 81.81% corresponded to vasculitis of small vessels. In 72,72%, the inflammatory component was neutrophils. 72,72% corresponded to Shönlein-Henoch purpura (PSH), 18,18% to Microscopic Polyangeitis (PAM), and 9,09% to Granulomatosis with Polyangeitis (GPA). In 72,72%, the treatment was Prednisone. Conclusion: Since this pathology is infrequent, with few studies that have studied its epidemiology, this work, with its limitations, could contribute for future studies.
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