Anestesia en paciente pediátrico con Síndrome de Treacher Collins

Walter Delgado Delgado Maidana; Raúl Eduardo Alonso; Ana Claudia De Barros

doi:10.18004/anales/2020.053.03.153

Authors

Walter Delgado Delgado Maidana Universidad Nacional de Asunción, Facultad de Ciencias Médicas, Departamento Central de Anestesiología. San Lorenzo, Paraguay. https://orcid.org/0000-0002-0494-7811
Raúl Eduardo Alonso Universidad Nacional de Asunción, Facultad de Ciencias Médicas, Departamento Central de Anestesiología. San Lorenzo, Paraguay. https://orcid.org/0000-0003-2289-0668
Ana Claudia De Barros Universidad Nacional de Asunción, Facultad de Ciencias Médicas, Departamento Central de Anestesiología. San Lorenzo, Paraguay. https://orcid.org/0000-0001-8104-7158

DOI:

https://doi.org/10.18004/anales/2020.053.03.153

Keywords:

Difficult Airway, Treacher Collins, Anesthesia, Pediatrics, Video Laryngoscope, Paraguay

Abstract

Treacher Collins Syndrome (TCS) constitutes a challenge for the anesthesiologist due to craniofacial malformations that make management of the airway and intubation difficult. We present a case of a patient (8-year-old) diagnosed with TCS who had to undergo surgery for the placement of a bone conduction implant under general anesthesia. She had a history of difficult intubation, marked micrognathia and a thyromental distance of 2 cm. An intubation scheme in two sequential stages was proposed. In the first stage, an evaluation of the airway (visualization of the glottis) was carried out under sedation with dexmedetomidine, remifentanil and propofol. When the glottis was visualized, we proceeded to the second stage to carry out intubation after anesthetic induction. The successful management of this case was based on adequate sedation and the use of a video laryngoscope with a curved blade for prior evaluation of the airway and subsequent intubation without complications.

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